A FATAL CASE OF 3-HYDROXYISOBUTYRYL-COA HYDROLASE DEFICIENCY IN A TERM INFANT WITH SEVERE HIGH ANION GAP ACIDOSIS AND REVIEW OF THE LITERATURE

A Fatal Case of 3-Hydroxyisobutyryl-CoA Hydrolase Deficiency in a Term Infant with Severe High Anion Gap Acidosis and Review of the Literature

3-hydroxy isobutyl-CoA hydrolase (HIBCH) deficiency is a T-Shirt recently described, rare inborn error of valine metabolism associated with a Leigh syndrome-like phenotype, neurodegenerative symptoms, and caused by recessive mutations in the HIBCH gene.We report the most severe case to date of an intrauterine growth-restricted term male who present

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MADRASA BY ANY OTHER NAME: Pondok, Pesantren, and Islamic Schools in Indonesia and Larger Southeast Asian Region

After more than a decade studying the Indonesian pesantren, the author had an opportunity to visit similar institutions in Thailand.After placing them in historical context, this paper explores how these Everything Else institutions vary in Southeast Asia.Although it is reasonable to presume that pondok between different countries and areas in the

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